Facial pilomatrix carcinomas treated with Mohs micrographic surgery

Pilomatrix carcinoma is a rare cutaneous malignancy with follicular matrix origin. Since the term pilomatrix carcinoma was first coined in 1980, more than 130 cases have been reported.1 The condition is also known as pilomatrical carcinoma, matrical carcinoma, malignant pilomatricoma, malignant pilomatrixoma, and calcifying epithelial carcinoma of Malherbe. In contrast to pilomatrixomas, pilomatrix carcinomas have locally aggressive behavior with a tendency toward recurrence and metastasis. Management options include surgery or radiation with close long-term follow-up.