A case of pediatric keratosis lichenoides chronica with unusual presentation of severe oral erosions

Keratosis lichenoides chronica (KLC) is a rare, chronic disorder of keratinization that typically affects adults.1 The adult-onset disease commonly presents with linear or reticular keratotic papules and plaques over the trunk and extremities, rosacea, or seborrheic dermatitis–like rash on the face and oral ulcers. Pediatric-onset KLC is rare with different clinical characteristics.2 Pediatric cases initially present with purpuric macules on the face, more commonly with alopecia of the forehead and eyebrows and less commonly affecting oral mucosa.