A Giant Congenital Mastoid Cholesteatoma With Extension to the Occipital Condyle

xlomafota13 shared this article with you from Inoreader A Giant Congenital Mastoid Cholesteatoma With Extension to the Occipital Condyle Via ear nose throat Ear Nose Throat J. 2021 Apr 18:1455613211007943. doi: 10.1177/01455613211007943. Online ahead of print. ABSTRACT A congenital mastoid cholesteatoma (CMC) is a keratinizing epithelium originating from embryological epithelial tissue of the mastoid. It is often not diagnosed until it becomes large because of its rarity and indolent nature. Although there are a few reports on giant CMC, its exact extensions have not been well described, and detailed information regarding surgic al methods is lacking, especially in giant CMC involving the occipital condyle and the middle and posterior cranial fossae. In this article, we report a case involving a 70-year-old woman with a giant CMC that extended inferiorly to the occipital condyle. The CMC eroded the middle and posterior cranial fossae, sigmoid sinus plate, and fallopian canal of the facial nerve. For complete removal, we used a subtotal petrosectomy in conjunction with an exposure of the cranial cervical junction and a wide decompression of the suboccipit. The boundaries of exposure were similar to those of a petro-occipital transsigmoid approach which is usually used for management of tumor involving the jugular foramen. The wide exposure allowed for complete removal of the lesion without any complications. Thus, we recommend this surgical approach for management of the giant CMC involving the occipital condyle and the middle and posterior cranial fossae. PMID:33866866 | DOI:10.1177/01455613211007943 View on the web Inoreader. Take back control of your news feed. Follow us on Twitter and Facebook.