Restrictive dermopathy: Report of two cases

Anisha K Janardhanan, Sarita Sasidharanpillai, Aparna S Vidya, Babu Francis, Mohandas Nair Karippoth

Indian Journal of Paediatric Dermatology 2018 19(4):360-362

Restrictive dermopathy is a rare entity that is fatal in the neonatal period itself. The rigidity of the skin leads to erosions, contractures, and restriction of respiratory movements. Diagnosis is often made clinically with classical features such as low-set ears, micrognathia, small, and persistently open fixed "o"-shaped mouth, translucent, shiny, rigid skin with prominent superficial blood vessels, and pseudocontractures of limb joints. We report two cases of restrictive dermopathy observed in our center within 2 years period and suggest that this condition may not be as rare as believed.