A fatal case of febrile ulceronecrotic mucha-habermann disease presenting as toxic epidermal necrolysis

Chenjing Xing, Hong Shen, Junzhu Xu, Zehu Liu, Jun Zhu, Aie Xu, Chenjing Xing, Hong Shen, Junzhu Xu, Zehu Liu, Jun Zhu, Aie Xu

Indian Journal of Dermatology 2017 62(6):675-675

Febrile ulceronecrotic Mucha-Habermann disease (FUMHD), a severe form of pityriasis lichenoides et varioliformis acuta, is an inflammatory dermatosis of unknown etiology manifested by ulcerative and necrotic lesions accompanied by systemic manifestations. The mortality rate of FUMHD is about 15%. It is reported here a case of FUMHD presenting as toxic epidermal necrolysis that resulted in multiple organ failure and death.