Malignant PEComa

We report a metastasizing PEComa in a pregnant 41-year-old female who had initially presented at her dermatologist during the first trimester of pregnancy with a newly developed indolent, slowly growing dermatofibroma-like tumor on the back of the left thigh. During pregnancy and after parturition, the lesion considerably progressed in size (Fig.1); tumor excision was performed 14 months after initial presentation.